| Stoffwechselstörung bzw. Porphyrie |
Urin |
Plasma |
Erythrozyten |
Stuhl |
| δ |
PG |
U |
VII |
VI |
V |
K |
III |
II |
U |
K |
P |
U |
K |
P |
U |
K |
P |
| kongenitale erythropoetische Porphyrie (M. Günther) |
n |
n |
↑↑ |
↑ |
↑ |
↑ |
↑↑ |
↑ |
↑ |
↑ |
↑ |
↑ |
↑↑ |
↑↑ |
↑ |
↑ |
↑ |
↑ |
| Erythrohepatische Porphyrie |
n |
n |
v |
n |
n |
v |
v |
v |
v |
n |
v |
↑ |
v |
v |
↑↑ |
n |
v |
↑ |
| Blei-Intoxikation, akut |
↑↑ |
v |
↑ |
↑ |
↑ |
↑↑ |
↑↑ |
↑↑ |
↑ |
n |
v |
v |
n |
n |
↑ |
n |
v |
v |
| Blei-Intoxikation, chronisch |
↑ |
n |
v |
v |
v |
↑ |
↑ |
↑ |
v |
n |
n |
v |
n |
n |
↑ |
n |
n |
v |
Porphobilinogen-
Synthetase-Defekt |
↑↑ |
v |
↑ |
↑ |
↑ |
↑↑ |
↑↑ |
↑↑ |
↑ |
n |
v |
v |
n |
n |
↑ |
n |
n |
n |
| akute intermittierende Porphyrie (AIP) |
↑↑ |
↑↑ |
↑↑ |
↑ |
↑ |
↑↑ |
↑↑ |
↑ |
↑ |
v |
v |
n |
n |
n |
v |
v |
v |
↑ |
| Porphyria variegata |
↑ |
↑ |
↑↑ |
↑ |
↑ |
↑↑ |
↑↑ |
↑ |
↑ |
v |
v |
v |
n |
n |
v |
v |
v |
↑↑ |
| heriditäre Koproporphyrien |
↑ |
↑ |
↑ |
↑ |
↑ |
↑↑ |
↑↑ |
↑ |
↑ |
n |
v |
n |
n |
n |
v |
v |
↑↑ |
↑ |
| chronisch hepatische Porphyrien (latent) |
n |
n |
↑ |
↑ |
v |
v |
↑ |
v |
n |
v |
v |
n |
v |
n |
n |
↑ |
v |
n |
| Porphyria cutanea tarda (PCT) |
v |
n |
↑↑ |
↑↑ |
↑ |
↑ |
↑ |
v |
n |
↑ |
v |
n |
v |
n |
n |
↑ |
v |
v |
| sekundäre Porphyrie bei asymptomatischer Koproporphyrinurie |
|
n |
v |
n |
n |
v |
↑ |
v |
n |
n |
v |
n |
n |
n |
v |
n |
v |
v |